NDUFB11 (NADH:Ubiquinone Oxidoreductase Subunit B11) is a Protein Coding gene. Diseases associated with NDUFB11 include Linear Skin Defects With Multiple Congenital Anomalies 3 and Mitochondrial Complex I Deficiency. Among its related pathways are Metabolism and Respiratory electron transport, ATP synthesis by chemiosmotic coupling, and heat production by uncoupling proteins. The protein encoded by NDUFB11 is a subunit of the multisubunit NADH:ubiquinone oxidoreductase (complex I). Mammalian complex I is located at the mitochondrial inner membrane. This protein has NADH dehydrogenase activity and oxidoreductase activity. It transfers electrons from NADH to ubiquinone.
