Isovaleryl-CoA dehydrogenase (IVD) is a mitochondrial matrix enzyme that catalyzes the third step in leucine catabolism. The genetic deficiency of IVD results in an accumulation of isovaleric acid, which is toxic to the central nervous system and leads to isovaleric acidemia. Alternatively spliced transcript variants encoding different isoforms have been found for this gene. [provided by RefSeq]
应用类型
该Anti-IVD产品的应用类型详情查看产品说明书。
免疫原
Full length human recombinant protein of human IVD (NP_002612) produced in HEK293T cell.
