MIPEP performs the final step in processing a specific class of nuclear-encoded proteins targeted to the mitochondrial matrix or inner membrane. This protein is primarily involved in the maturation of oxidative phosphorylationn(OXPHOS)-related proteins. It may contribute to the functional effects of frataxin deficiency and the clinical manifestations of Friedreich ataxia.
应用类型
WB,IHC
免疫原
This MIPEP antibody is generated from rabbits immunized with a KLH conjugated synthetic peptide between 307-336 amino acids from the Central region of human MIPEP.