The protein encoded by this gene is a nuclear protein which is transported to the mitochondrial inner membrane. Together with carnitine palmitoyltransferase I, the encoded protein oxidizes long-chain fatty acids in the mitochondria. Defects in this gene are associated with mitochondrial long-chain fatty-acid (LCFA) oxidation disorders.
应用类型
WB,FCM
免疫原
Purified recombinant fragment of human CPT2 (AA: 26-178) expressed in E. Coli.