This gene encodes a mitochondrial 3-hydroxyisobutyrate dehydrogenase enzyme. The encoded protein plays a critical role in the catabolism of L-valine by catalyzing the oxidation of 3-hydroxyisobutyrate to methylmalonate semialdehyde.
应用类型
WB, IHC, IF/ICC
免疫原
Recombinant fusion protein of human HIBADH(NP_689953.1).