NDUFV1 (NADH:Ubiquinone Oxidoreductase Core Subunit V1) is a Protein Coding gene. Diseases associated with NDUFV1 include Mitochondrial Complex I Deficiency and Leigh Syndrome With Leukodystrophy. Among its related pathways are Metabolism and Respiratory electron transport, ATP synthesis by chemiosmotic coupling, and heat production by uncoupling proteins.