ACADS (acyl-Coenzyme A dehydrogenase),is a homotetrameric mitochondrial flavoprotein that belongs to the acyl-CoA dehydrogenase family. This enzyme catalyzes the initial step of the mitochondrial fatty acid beta-oxidation pathway. Mutation of this gene causes SCAD deficiency an acute acidosis and muscle weakness in infants and lipid-storage myopathy in adults.
应用类型
Western Blot analysis (1-4 µg/ml).
免疫原
Synthetic peptide surrounding amino acid 380 of rat ACADS
来源宿主
兔
反应性
经检测验证,可与人、小鼠、大鼠种属来源的ACADS蛋白发生免疫反应.
保存建议
提供的ACADS抗体为无色溶液形式,产品浓度为0.5 mg/ml,溶解于包含有30%甘油, 0.5% BSA, 5 mM EDTA和0.01%硫柳汞的PBS缓冲液(pH 7.2)中.请在收到该ACADS抗体产品后,将其置于-20 °C冷冻保存,建议分装使用以避免反复冻融.