Lipoamide Dehydrogenase encodes the L protein of the mitochondrial glycine cleavage system. Mutations in this gene have been identified in patients with E3-deficient maple syrup urine disease and lipoamide dehydrogenase deficiency.
应用类型
ELISA,Immunoprecipitation,Western Blot,
免疫原
Lipoamide Dehydrogenase [Porcine Heart]
来源宿主
Rabbit
反应性
Sus scrofa domesticus (Pig, Porcine, Swine)
保存建议
Store vial at 4° C prior to restoration. For extended storage aliquot contents and freeze at -20° C or below. Avoid cycles of freezing and thawing. Centrifuge product if not completely clear after standing at room temperature. This product is stable for several weeks at 4° C as an undiluted liquid. Dilute only prior to immediate use.
